Хирургическое лечение липоменингоцеле у детей (Обзор литературы)
Аннотация
Липоменингоцеле - вариант скрытой формы спинального дизрафизма, при котором в процессе эмбриогенеза не происходит полного разделения между нейроэктодермой и мезенхимальными элементами, формирующими позвоночник и мягкие ткани вокруг нервной трубки. Частота встречаемости составляет 1:4000 новорождённых, что составляетт 60% от всех липом спинного мозга. В зависимости от анатомических взаимоотношений липом со спинным мозгом выделяют следующие формы: дорзальная липома, каудальная липома, переходная липома. По отношению к твёрдой мозговой оболочке и позвоночного канала разделяют на интрадуральную, интра,-экстрадуральную. Стратегии лечения варьируются в зависимости от подтипа, неврологического дефицита и методов операции.
Данная статья представляет собой обзор литературы посвященной оценкам и результатам хирургического лечения липомененгоцеле у детей.
Ключевые слова:
Об авторах
Список литературы
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Conclusions
Lipomeningocele is a form of closed neural tube defect with unclear predisposing factors. Due to the risk of worsening neurological and urological function secondary to a tethered spinal cord, it continues to be important to identify this condition for timely intervention. Magnetic resonance im-aging and neurophysiological testing are useful tools for iden¬tifying the spinal cord pathology and assisting with surgical planning. Because bowel and bladder paresis remains the pri¬mary morbidity of this disease, early intervention either prior to symptom development, or at the first onset of symptoms, is recommended to optimize postoperative outcome.
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